Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome

Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome

Blog Article

Marfan syndrome is an inherited, connective-tissue disorder transmitted as an autosomal dominant trait.Cardinal Leather Keychain features of the disorder include tall stature, ectopia lentis, mitral valve prolapse, aortic root dilatation, and aortic dissection.Pectus excavatum may exist as an isolated lesion or in association with a genetic syndrome such Bridal as Marfan syndrome.

We report the successful management of a simultaneous correction of pectus excavatum and the underlying cardiovascular diseases.